Quinolinic Acid

Overview

Quinolinic acid is an endogenous metabolite of the kynurenine pathway from tryptophan degradation, measured in cerebrospinal fluid (CSF), plasma, or urine as a marker of neuroinflammation and excitotoxicity. It acts as an agonist of NMDA receptors, contributing to neuronal damage in neurodegenerative and inflammatory conditions. Elevated levels indicate central nervous system inflammation, HIV-associated neurocognitive disorders, or ischemia, while low levels lack established clinical significance; it is primarily useful in research for monitoring neuroinflammatory diseases and assessing excitotoxic risk.

Clinical Use Cases

  • Research biomarker for neuroinflammation in multiple sclerosis.
  • Assessing HIV-related neurocognitive impairment.
  • Investigating excitotoxicity in stroke or traumatic brain injury.
  • Studying Huntington's disease progression.
  • Evaluating kynurenine pathway activation in psychiatric disorders.

Specimen Types

  • Cerebrospinal fluid (primary for CNS assessment).
  • Plasma or serum.
  • Urine.

Measurement Methods

  • Liquid chromatography-tandem mass spectrometry (LC-MS/MS).
  • High-performance liquid chromatography (HPLC) with fluorescence or electrochemical detection.
  • Gas chromatography-mass spectrometry (GC-MS).
  • Enzymatic assays (research use).

Test Preparation and Influencing Factors

  • No specific fasting required.
  • Avoid lumbar puncture delays for CSF stability.
  • Influenced by inflammation, infections, or interferon-gamma induction.
  • Tryptophan intake or IDO inhibitors may alter levels.
  • Sample processing critical: freeze immediately at -80°C.

Synonyms

  • QUIN.
  • Pyridine-2,3-dicarboxylic acid.
  • Quinolinic acid (neurotoxic kynurenine metabolite).

Further Reading